Amyotrophic lateral sclerosis (ALS), or Lou Gehrig’s disease, is a neurodegenerative disease resulting in the progressive loss of motor neurons that control voluntary muscles. ALS is a neurological disease that primarily affects the nerve cells (neurons) responsible for controlling voluntary muscle movement. Voluntary muscles generate movements like chewing, walking, and talking. The disease is progressive as the symptoms get considerably worse as time continues. As of today, there is no cure for ALS and no effective treatment to halt or reverse the progression of the disease.

ALS belongs to a wider group of disorders known as motor neuron diseases, which are caused by the gradual deterioration and death of motor neurons. Motor neurons are nerve cells that extend from the brain to the spinal cord and to muscles throughout the body. As motor neurons degenerate, they stop sending messages to the muscles, and the muscles gradually atrophy. Ultimately, the brain loses its ability to initiate and control voluntary movements.

As mobility continues to decline, most patients will need a power wheelchair… Proper seating and positioning are essential to ensure a comfortable and functional sitting posture, allow for maximal breathing capacity, and prevent secondary injuries, such as skin breakdown and back pain. Transitioning to power mobility may require a number of corresponding environmental modifications, because power wheelchairs do not fit into narrow doorways and standard cars. Ramps are needed to enter the home if there are steps, and a modified van is needed for transportation. 

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